지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 저널정보
- 뮤코다당증연구학회 Journal of mucopolysaccharidosis and rare disease Journal of mucopolysaccharidosis and rare disease 제1권 제2호
- 발행연도
- 2015.1
- 수록면
- 44 - 48 (5page)
이용수
초록· 키워드
오류제보하기
Body fat distribution in patients with Prader-Willi syndrome (PWS) is characterized by reduce lean body mass (LBM), increased total body fat mass (FM), and lower percentage of visceral adipose tissue (VAT). Individuals with PWS seem to have a lower risk for insulin resistance with high levels of adiponectin, an anti-atherogenic adipocytokine that is decreased in visceral fat hypertrophy subjects compared to simple obese subjects, both in children and in adults. The mechanism of the reduction in visceral adiposity in PWS is still unclear. It might be related to qualitative intrinsic characteristics of adipocyte or novel genetic influences on the control of fat distribution. However, obesity remains a critical problem, and obesity status plays a crucial role in individual metabolic risk clustering and development of metabolic syndrome (Mets) in PWS children and adults. Long-term growth hormone (GH) treatment after cessation of skeletal growth improved body composition, with an increase in lean body mass and a reduction in total body fat and subcutaneous and visceral fat in PWS adults. Thus, the role of GH is important after childhood because it might attenuate obesity and Mets in PWS adult by adipocyte modification.
목차
등록된 정보가 없습니다.
참고문헌 (0)
참고문헌 신청함께 읽어보면 좋을 논문
논문 유사도에 따라 DBpia 가 추천하는 논문입니다. 함께 보면 좋을 연관 논문을 확인해보세요!
-
Issues in Adults Prader-Willi Syndrome
Journal of mucopolysaccharidosis and rare disease
2015 .01
-
Growth Hormone Therapy in Adults with Prader-Willi Syndrome
Journal of mucopolysaccharidosis and rare disease
2015 .01
-
Prader-Willi syndrome: an update on obesity and endocrine problems
Annals of Pediatirc Endocrinology & Metabolism
2021 .12
-
An Update on Prader-Willi Syndrome with Diabetes Mellitus
Journal of mucopolysaccharidosis and rare disease
2016 .01
-
Genetics of Prader-Willi syndrome and Prader-Will-Like syndrome
Annals of Pediatirc Endocrinology & Metabolism
2016 .01
-
Beneficial Effects of Growth Hormone Treatment in Prader-Willi Syndrome
Journal of mucopolysaccharidosis and rare disease
2017 .01
-
Quality of Life in Prader-Willi Syndrome Patients
Journal of mucopolysaccharidosis and rare disease
2015 .01
-
Gene Expression Related to Cognitive Function in Growth Hormone-treated Mice with Prader-Willi Syndrome
Journal of mucopolysaccharidosis and rare disease
2016 .01
-
Evaluating the Efficacy of Pharmacological Therapy for Prader-Willi Syndrome: A Systematic Review and Meta-analysis
한국임상약학회지
2022 .12
-
An 18-year-old patient with Prader-Willi syndrome: a case report on dental management under sedation and general anesthesia
Journal of dental anesthesia and pain medicine
2015 .01
-
Successful rapid weight reduction and the use of liraglutide for morbid obesity in adolescent Prader-Willi syndrome
Annals of Pediatirc Endocrinology & Metabolism
2020 .01
-
Impact of Visceral Obesity on the Risk of Incident Metabolic Syndrome in Metabolically Healthy Normal Weight and Overweight Groups: A Longitudinal Cohort Study in Korea
Korean Journal of Family Medicine
2020 .01
-
Introduction to the New Version of PWS Application and It's Use in Medical Practice
Journal of mucopolysaccharidosis and rare disease
2016 .01
-
Tailored management of life-threatening complications related to severe obesity in a young adult with Prader-Willi syndrome
Annals of Pediatirc Endocrinology & Metabolism
2022 .06
-
Clinical Usefulness of Aripiprazole Treatment in a Girl with Prader-Willi Syndrome and Psychosis
Clinical Psychopharmacology and Neuroscience
2018 .01
-
Birth seasonality in Korean Prader-Willi syndrome with chromosome 15 microdeletion
Annals of Pediatirc Endocrinology & Metabolism
2015 .01
-
프래더-윌리 증후군을 가진 46개월 소아의 치과치료 : 증례보고
International Journal of Disability and Oral Health
2019 .06
-
The Effect of Growth Hormone on mRNA Expression of the GABA<sub>B1</sub> Receptor Subunit and GH/IGF Axis Genes in a Mouse Model of Prader-Willi Syndrome
Journal of mucopolysaccharidosis and rare disease
2015 .01
-
Growth Hormone Therapy in PWS with Mobile Application-Living with PWS
Journal of mucopolysaccharidosis and rare disease
2018 .01
-
Being Metabolically Healthy, the Most Responsible Factor for Vascular Health
Diabetes and Metabolism Journal
2018 .01
이 논문의 저자 정보
최근 본 자료
댓글(0)
0