지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2017.1
- 수록면
- 476 - 478 (3page)
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초록· 키워드
오류제보하기
X-linked agammaglobulinemia (XLA) is a primary immunodeficiency disorder caused by germline mutations of B-cell tyrosine kinase (BTK) gene. It is characterized by decreased serum immunoglobulins levels and circulating mature B cells. This defect in humoral immunity leads to increased susceptibility to infection. Pyoderma gangrenosum (PG) is an uncommon, ulcerating, neutrophilic dermatosis.
Here we report PG in an 8-year-old patient with XLA. The patient received intravenous immunoglobulin treatment in conjunction with prednisone and topical application of 0.03% tacrolimus ointment and the ulcer was almost completely healed in the 2 weeks of follow-up. The coexistence has been rarely reported. XLA may be a possible cofactor in the pathogenesis of PG.
목차
등록된 정보가 없습니다.
참고문헌 (14)
참고문헌 신청
Adachi Y / 1998 / Aberrant neutrophil trafficking and metabolic oscillations in severe pyoderma gangrenosum / J Invest Dermatol 111 : 259 ~ 268
Barriere H / 1979 / Pyoderma gangrenosum associated with congenital hypogammaglobulin / Ann Dermatol Venereol 106 : 695 ~ 696
Bloom D / 1958 / Pyoderma gangrenosum associated with hypogammaglobulinemia; report of two cases / AMA Arch Derm 77 : 412 ~ 421
Bruton OC / 1952 / Agammaglobulinemia / Pediatrics 9 : 722 ~ 728
Cafardi J / 2014 / Intravenous immunoglobulin as salvage therapy in refractory pyoderma gangrenosum: report of a case and review of the literature / Case Rep Dermatol 6 : 23
Barriere H / 1979 / Pyoderma gangrenosum associated with congenital hypogammaglobulin / Ann Dermatol Venereol 106 : 695 ~ 696
Bloom D / 1958 / Pyoderma gangrenosum associated with hypogammaglobulinemia; report of two cases / AMA Arch Derm 77 : 412 ~ 421
Bruton OC / 1952 / Agammaglobulinemia / Pediatrics 9 : 722 ~ 728
Cafardi J / 2014 / Intravenous immunoglobulin as salvage therapy in refractory pyoderma gangrenosum: report of a case and review of the literature / Case Rep Dermatol 6 : 23
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